Start Date

2018

Description

  • Establish a yeast model system for the study of BCS1L function.
  • Develop assays to investigate differences in mitochondrial efficiency and electron transport chain functionality of BCS1L mutants.
  • Connect hearing-loss associated BCS1L mutations to mitochondrial structure and function to better explain the clinical variation observed in patients with BCS1L mutations

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Jan 1st, 12:00 AM

Elucidating Genotype-Phenotype Relationships in BCS1L Mutations

  • Establish a yeast model system for the study of BCS1L function.
  • Develop assays to investigate differences in mitochondrial efficiency and electron transport chain functionality of BCS1L mutants.
  • Connect hearing-loss associated BCS1L mutations to mitochondrial structure and function to better explain the clinical variation observed in patients with BCS1L mutations